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INTERNATIONAL CLASSIFICATION OF DISEASES

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vertical line Table of Contents Alphabetical Index of Diseases and Injuries Explanation of Disease Classification

8. Diseases of the Respiratory System (460-519)




Use additional code to identify infectious organism

ACUTE RESPIRATORY INFECTIONS (460-466)

Excludes:	pneumonia and influenza (480.0-488)
460	Acute nasopharyngitis [common cold]
Coryza (acute)
Nasal catarrh, acute
Nasopharyngitis:
NOS
acute
infective NOS
Rhinitis:
acute
infective
Excludes:	nasopharyngitis, chronic (472.2)
pharyngitis:
acute or unspecified (462)
chronic (472.1)
rhinitis:
allergic (477.0-477.9)
chronic or unspecified (472.0)
sore throat:
acute or unspecified (462)
chronic (472.1)
461	Acute sinusitis
Includes:	abscess, acute, of sinus (accessory) (nasal)
empyema, acute, of sinus (accessory) (nasal)
infection, acute, of sinus (accessory) (nasal)
inflammation, acute, of sinus (accessory) (nasal)
suppuration, acute, of sinus (accessory) (nasal)
Excludes:	chronic or unspecified sinusitis (473.0-473.9)
461.0	Maxillary
Acute antritis
461.1	Frontal
461.2	Ethmoidal
461.3	Sphenoidal
461.8	Other acute sinusitis
Acute pansinusitis
461.9	Acute sinusitis, unspecified
Acute sinusitis NOS
462	Acute pharyngitis
Acute sore throat NOS
Pharyngitis (acute):
NOS
gangrenous
infective
phlegmonous
pneumococcal
staphylococcal
suppurative
ulcerative
Sore throat (viral) NOS
Viral pharyngitis
Excludes:	abscess:
peritonsillar [quinsy] (475)
pharyngeal NOS (478.29)
retropharyngeal (478.24)
chronic pharyngitis (472.1)
infectious mononucleosis (075)
that specified as (due to):
Coxsackie (virus) (074.0)
gonococcus (098.6)
herpes simplex (054.79)
influenza (487.1)
septic (034.0)
streptococcal (034.0)
463	Acute tonsillitis
Tonsillitis (acute):
NOS
follicular
gangrenous
infective
pneumococcal
septic
staphylococcal
suppurative
ulcerative
viral
Excludes:	chronic tonsillitis (474.0)
hypertrophy of tonsils (474.1)
peritonsillar abscess [quinsy] (475)
sore throat:
acute or NOS (462)
septic (034.0)
streptococcal tonsillitis (034.0)
464	Acute laryngitis and tracheitis
Excludes:	that associated with influenza (487.1)
that due to Streptococcus (034.0)
464.0	Acute laryngitis
Laryngitis (acute):
NOS
edematous
Hemophilus influenzae [H. influenzae]
pneumococcal
septic
suppurative
ulcerative
Excludes:	chronic laryngitis (476.0-476.1)
influenzal laryngitis (487.1)
464.00	Without mention of obstruction
464.01	With obstruction
464.1	Acute tracheitis
Tracheitis (acute):
NOS
catarrhal
viral
Excludes:	chronic tracheitis (491.8)
464.10	Without mention of obstruction
464.11	With obstruction
464.2	Acute laryngotracheitis
Laryngotracheitis (acute)
Tracheitis (acute) with laryngitis (acute)
Excludes:	chronic laryngotracheitis (476.1)
464.20	Without mention of obstruction
464.21	With obstruction
464.3	Acute epiglottitis
Viral epiglottitis
Excludes:	epiglottitis, chronic (476.1)
464.30	Without mention of obstruction
464.31	With obstruction
464.4	Croup
Croup syndrome
464.5	Supraglottitis, unspecified
464.50	Without mention of obstruction
464.51	With obstruction
465	Acute upper respiratory infections of multiple or unspecified sites
Excludes:	upper respiratory infection due to:
influenza (487.1)
Streptococcus (034.0)
465.0	Acute laryngopharyngitis
465.8	Other multiple sites
Multiple URI
465.9	Unspecified site
Acute URI NOS
Upper respiratory infection (acute)
466	Acute bronchitis and bronchiolitis
Includes:	that with:
bronchospasm
obstruction
466.0	Acute bronchitis
Bronchitis, acute or subacute:
fibrinous
membranous
pneumococcal
purulent
septic
viral
with tracheitis
Croupous bronchitis
Tracheobronchitis, acute
Excludes:	acute bronchitis with chronic obstructive pulmonary disease (491.22)
466.1	Acute bronchiolitis
Bronchiolitis (acute)
Capillary pneumonia
466.11	Acute bronchiolitis due to respiratory syncytial virus (RSV)
466.19	Acute bronchiolitis due to other infectious organisms
Use additional code to identify organism

OTHER DISEASES OF THE UPPER RESPIRATORY TRACT (470-478)

470	Deviated nasal septum
Deflected septum (nasal) (acquired)
Excludes:	congenital (754.0)
471	Nasal polyps
Excludes:	adenomatous polyps (212.0)
471.0	Polyp of nasal cavity
Polyp:
choanal
nasopharyngeal
471.1	Polypoid sinus degeneration
Woakes' syndrome or ethmoiditis
471.8	Other polyp of sinus
Polyp of sinus:
accessory
ethmoidal
maxillary
sphenoidal
471.9	Unspecified nasal polyp
Nasal polyp NOS
472	Chronic pharyngitis and nasopharyngitis
472.0	Chronic rhinitis
Ozena
Rhinitis:
NOS
atrophic
granulomatous
hypertrophic
obstructive
purulent
ulcerative
Excludes:	allergic rhinitis (477.0-477.9)
472.1	Chronic pharyngitis
Chronic sore throat
Pharyngitis:
atrophic
granular (chronic)
hypertrophic
472.2	Chronic nasopharyngitis
Excludes:	acute or unspecified nasopharyngitis (460)
473	Chronic sinusitis
Includes:	abscess (chronic) of sinus (accessory) (nasal)
empyema (chronic) of sinus (accessory) (nasal)
infection (chronic) of sinus (accessory) (nasal)
suppuration (chronic) of sinus (accessory) (nasal)
Excludes:	acute sinusitis (461.0-461.9)
473.0	Maxillary
Antritis (chronic)
473.1	Frontal
473.2	Ethmoidal
Excludes:	Woakes' ethmoiditis (471.1)
473.3	Sphenoidal
473.8	Other chronic sinusitis
Pansinusitis (chronic)
473.9	Unspecified sinusitis (chronic)
Sinusitis (chronic) NOS
474	Chronic disease of tonsils and adenoids
474.0	Chronic tonsillitis and adenoiditis
Excludes:	acute or unspecified tonsillitis (463)
474.00	Chronic tonsillitis
474.01	Chronic adenoiditis
474.02	Chronic tonsillitis and adenoiditis
474.1	Hypertrophy of tonsils and adenoids
Enlargement of tonsils or adenoids
Hyperplasia of tonsils or adenoids
Hypertrophy of tonsils or adenoids
Excludes:	that with:
adenoiditis (474.01)
adenoiditis and tonsillitis (474.02)
tonsillitis (474.00)
474.10	Tonsils with adenoids
474.11	Tonsils alone
474.12	Adenoids alone
474.2	Adenoid vegetations
474.8	Other chronic disease of tonsils and adenoids
Amygdalolith
Calculus, tonsil
Cicatrix of tonsil (and adenoid)
Tonsillar tag
Ulcer, tonsil
474.9	Unspecified chronic disease of tonsils and adenoids
Disease (chronic) of tonsils (and adenoids)
475	Peritonsillar abscess
Abscess of tonsil
Peritonsillar cellulitis
Quinsy
Excludes:	tonsillitis:
acute or NOS (463)
chronic (474.0)
476	Chronic laryngitis and laryngotracheitis
476.0	Chronic laryngitis
Laryngitis:
catarrhal
hypertrophic
sicca
476.1	Chronic laryngotracheitis
Laryngitis, chronic, with tracheitis (chronic)
Tracheitis, chronic, with laryngitis
Excludes:	chronic tracheitis (491.8)
laryngitis and tracheitis, acute or unspecified (464.00-464.51)
477	Allergic rhinitis
Includes:	allergic rhinitis (nonseasonal) (seasonal)
hay fever
spasmodic rhinorrhea
Excludes:	allergic rhinitis with asthma (bronchial) (493.0)
477.0	Due to pollen
Pollinosis
477.1	Due to food
477.2	Due to animal (cat) (dog) hair and dander
477.8	Due to other allergen
477.9	Cause unspecified
478	Other diseases of upper respiratory tract
478.0	Hypertrophy of nasal turbinates
478.1	Other diseases of nasal cavity and sinuses
Excludes:	varicose ulcer of nasal septum (456.8)
478.11	Nasal mucositis (ulcerative)
Use additional E code to identify adverse effects of therapy, such as:
antineoplastic and immunosuppressive drugs (E930.7, E933.1)
radiation therapy (E879.2)
478.19	Other disease of nasal cavity and sinuses
Abscess of nose (septum)
Necrosis of nose (septum)
Ulcer of nose (septum)
Cyst or mucocele of sinus (nasal)
Rhinolith
478.2	Other diseases of pharynx, not elsewhere classified
478.20	Unspecified disease of pharynx
478.21	Cellulitis of pharynx or nasopharynx
478.22	Parapharyngeal abscess
478.24	Retropharyngeal abscess
478.25	Edema of pharynx or nasopharynx
478.26	Cyst of pharynx or nasopharynx
478.29	Other
Abscess of pharynx or nasopharynx
Excludes:	ulcerative pharyngitis (462)
478.3	Paralysis of vocal cords or larynx
478.30	Paralysis, unspecified
Laryngoplegia
Paralysis of glottis
478.31	Unilateral, partial
478.32	Unilateral, complete
478.33	Bilateral, partial
478.34	Bilateral, complete
478.4	Polyp of vocal cord or larynx
Excludes:	adenomatous polyps (212.1)
478.5	Other diseases of vocal cords
Abscess of vocal cords
Cellulitis of vocal cords
Granuloma of vocal cords
Leukoplakia of vocal cords
Chorditis (fibrinous) (nodosa) (tuberosa)
Singers' nodes
478.6	Edema of larynx
Edema (of):
glottis
subglottic
supraglottic
478.7	Other diseases of larynx, not elsewhere classified
478.70	Unspecified disease of larynx
478.71	Cellulitis and perichondritis of larynx
478.74	Stenosis of larynx
478.75	Laryngeal spasm
Laryngismus (stridulus)
478.79	Other
Abscess of larynx
Necrosis of larynx
Obstruction of larynx
Pachyderma of larynx

Ulcer of larynx
Excludes:	ulcerative laryngitis (464.00-464.01)
478.8	Upper respiratory tract hypersensitivity reaction, site unspecified
Excludes:	hypersensitivity reaction of lower respiratory tract, as:
extrinsic allergic alveolitis (495.0-495.9)
pneumoconiosis (500-505)
478.9	Other and unspecified diseases of upper respiratory tract
Abscess of trachea
Cicatrix of trachea

PNEUMONIA AND INFLUENZA (480-488)

Excludes:	pneumonia:
allergic or eosinophilic (518.3)
aspiration:
NOS (507.0)
newborn (770.18)
solids and liquids (507.0-507.8)
congenital (770.0)
lipoid (507.1)
passive (514)
rheumatic (390)
480	Viral pneumonia
480.0	Pneumonia due to adenovirus
480.1	Pneumonia due to respiratory syncytial virus
480.2	Pneumonia due to parainfluenza virus
480.3	Pneumonia due to SARS-associated coronavirus
480.8	Pneumonia due to other virus not elsewhere classified
Excludes:	congenital rubella pneumonitis (771.0)
influenza with pneumonia, any form (487.0)
pneumonia complicating viral diseases classified elsewhere (484.1-484.8)
480.9	Viral pneumonia, unspecified
481	Pneumococcal pneumonia [Streptococcus pneumoniae pneumonia]
Lobar pneumonia, organism unspecified
482	Other bacterial pneumonia
482.0	Pneumonia due to Klebsiella pneumoniae
482.1	Pneumonia due to Pseudomonas
482.2	Pneumonia due to Hemophilus influenzae [H. influenzae]
482.3	Pneumonia due to Streptococcus
Excludes:	Streptococcus pneumoniae pneumonia (481)
482.30	Streptococcus, unspecified
482.31	Group A
482.32	Group B
482.39	Other Streptococcus
482.4	Pneumonia due to Staphylococcus
482.40	Pneumonia due to Staphylococcus, unspecified
482.41	Pneumonia due to Staphylococcus aureus
482.49	Other Staphylococcus pneumonia
482.8	Pneumonia due to other specified bacteria
Excludes: pneumonia complicating infectious disease classified elsewhere (484.1-484.8)
482.81	Anaerobes
Gram-negative anaerobes
Bacteroides (melaninogenicus)
482.82	Escherichia coli [E. coli]
482.83	Other gram-negative bacteria
Gram-negative pneumonia NOS
Proteus
Serratia marcescens
Excludes:	gram-negative anaerobes (482.81)
Legionnaires' disease (482.84)
482.84	Legionnaires' disease
482.89	Other specified bacteria
482.9	Bacterial pneumonia unspecified
483	Pneumonia due to other specified organism
483.0	Mycoplasma pneumoniae
Eaton's agent
Pleuropneumonia-like organisms [PPLO]
483.1	Chlamydia
483.8	Other specified organism
484	Pneumonia in infectious diseases classified elsewhere
Excludes:	influenza with pneumonia, any form (487.0)
484.1	Pneumonia in cytomegalic inclusion disease
Code first underlying disease, as: (078.5)
484.3	Pneumonia in whooping cough
Code first underlying disease, as: (033.0-033.9)
484.5	Pneumonia in anthrax
Code first underlying disease (022.1)
484.6	Pneumonia in aspergillosis
Code first underlying disease (117.3)
484.7	Pneumonia in other systemic mycoses
Code first underlying disease
Excludes:	pneumonia in:
candidiasis (112.4)
coccidioidomycosis (114.0)
histoplasmosis (115.0-115.9 with fifth-digit 5)
484.8	Pneumonia in other infectious diseases classified elsewhere
Code first underlying disease, as:
Q fever (083.0)
typhoid fever (002.0)
Excludes:	pneumonia in:
actinomycosis (039.1)
measles (055.1)
nocardiosis (039.1)
ornithosis (073.0)
Pneumocystis carinii (136.3)
salmonellosis (003.22)
toxoplasmosis (130.4)
tuberculosis (011.6)
tularemia (021.2)
varicella (052.1)
485	Bronchopneumonia, organism unspecified
Bronchopneumonia:
hemorrhagic
terminal
Pleurobronchopneumonia
Pneumonia:
lobular
segmental
Excludes:	bronchiolitis (acute) (466.11- 466.19)
chronic (491.8)
lipoid pneumonia (507.1)
486	Pneumonia, organism unspecified
Excludes:	hypostatic or passive pneumonia (514)
influenza with pneumonia, any form (487.0)
inhalation or aspiration pneumonia due to foreign materials (507.0-507.8)
pneumonitis due to fumes and vapors (506.0)
487	Influenza
Excludes:	Hemophilus influenzae [H. influenzae]:
infection NOS (041.5)
laryngitis (464.00-464.01)
meningitis (320.0)
influenza due to identified avian influenza virus (488)
487.0	With pneumonia
Influenza with pneumonia, any form
Influenzal:
bronchopneumonia
pneumonia
Use additional code to identify the type of pneumonia (480.0-480.9, 481, 482.0-482.9,
 483.0-483.8, 485)
487.1	With other respiratory manifestations
Influenza NOS
Influenzal:
laryngitis
pharyngitis
respiratory infection (upper) (acute)
487.8	With other manifestations
Encephalopathy due to influenza
Influenza with involvement of gastrointestinal tract
Excludes:	"intestinal flu" [viral gastroenteritis] (008.8)
488	Influenza due to identified avian influenza virus
Note:	Influenza caused by influenza viruses that normally infect only birds and, less
 commonly, other animals
Excludes:	influenza caused by other influenza viruses (487)

CHRONIC OBSTRUCTIVE PULMONARY DISEASE AND ALLIED CONDITIONS (490-496)

490	Bronchitis, not specified as acute or chronic
Bronchitis NOS:
catarrhal
with tracheitis NOS
Tracheobronchitis NOS
Excludes:	bronchitis:
allergic NOS (493.9)
asthmatic NOS (493.9)
due to fumes and vapors (506.0)
491	Chronic bronchitis
Excludes:	chronic obstructive asthma (493.2)
491.0	Simple chronic bronchitis
Catarrhal bronchitis, chronic
Smokers' cough
491.1	Mucopurulent chronic bronchitis
Bronchitis (chronic) (recurrent):
fetid
mucopurulent
purulent
491.2	Obstructive chronic bronchitis
Bronchitis:
emphysematous
obstructive (chronic) (diffuse)
Bronchitis with:
chronic airway obstruction
emphysema
Excludes:	asthmatic bronchitis (acute) (NOS) 493.9
chronic obstructive asthma 493.2
491.20	Without exacerbation
Emphysema with chronic bronchitis
491.21	With (acute) exacerbation
Acute exacerbation of chronic obstructive pulmonary disease [COPD]
Decompensated chronic obstructive pulmonary disease [COPD]
Decompensated chronic obstructive pulmonary disease [COPD] with exacerbation
Excludes:	chronic obstructive asthma with acute exacerbation 493.22
491.22	With acute bronchitis
491.8	Other chronic bronchitis
Chronic:
tracheitis
tracheobronchitis
491.9	Unspecified chronic bronchitis
492	Emphysema
492.0	Emphysematous bleb
Giant bullous emphysema
Ruptured emphysematous bleb
Tension pneumatocele
Vanishing lung
492.8	Other emphysema
Emphysema (lung or pulmonary):
NOS
centriacinar
centrilobular
obstructive
panacinar
panlobular
unilateral
vesicular
MacLeod's syndrome
Swyer-James syndrome
Unilateral hyperlucent lung
Excludes:	emphysema:
with chronic bronchitis (491.20-491.22)
compensatory (518.2)
due to fumes and vapors (506.4)
interstitial (518.1)
newborn (770.2)
mediastinal (518.1)
surgical (subcutaneous) (998.81)
traumatic (958.7)
493	Asthma
Excludes:	wheezing NOS (786.07)
The following fifth-digit subclassification is for use with category 493.0-493.2, 493.9:
0	unspecified
1	with status asthmaticus
2	with (acute) exacerbation
493.0	Extrinsic asthma
Asthma:
allergic with stated cause
atopic
childhood
hay
platinum
Hay fever with asthma
Excludes:	asthma:
allergic NOS (493.9)
detergent (507.8)
miners' (500)
wood (495.8)
493.1	Intrinsic asthma
Late-onset asthma
493.2	Chronic obstructive asthma
Asthma with chronic obstructive pulmonary disease [COPD]
Chronic asthmatic bronchitis
Excludes:	acute bronchitis (466.0)
chronic obstructive bronchitis (491.20-491.22)
493.8	Other forms of asthma
493.81	Exercise induced bronchospasm
493.82	Cough variant asthma
493.9	Asthma, unspecified
Asthma (bronchial) (allergic NOS)
Bronchitis:
allergic
asthmatic
494	Bronchiectasis
Bronchiectasis (fusiform) (postinfectious) (recurrent)
Bronchiolectasis
Excludes:	congenital (748.61)
tuberculous bronchiectasis (current disease) (011.5)
494.0	Bronchiectasis without acute exacerbation
494.1	Bronchiectasis with acute exacerbation
495	Extrinsic allergic alveolitis
Includes:	allergic alveolitis and pneumonitis due to inhaled organic dust particles
 of fungal, thermophilic actinomycete, or other origin
495.0	Farmers' lung
495.1	Bagassosis
495.2	Bird-fanciers' lung
Budgerigar-fanciers' disease or lung
Pigeon-fanciers' disease or lung
495.3	Suberosis
Cork-handlers' disease or lung
495.4	Malt workers' lung
Alveolitis due to Aspergillus clavatus
495.5	Mushroom workers' lung
495.6	Maple bark-strippers' lung
Alveolitis due to Cryptostroma corticale
495.7	"Ventilation" pneumonitis
Allergic alveolitis due to fungal, thermophilic actinomycete, and other organisms growing
 in ventilation [air conditioning] systems
495.8	Other specified allergic alveolitis and pneumonitis
Cheese-washers' lung
Coffee workers' lung
Fish-meal workers' lung
Furriers' lung
Grain-handlers' disease or lung
Pituitary snuff-takers' disease
Sequoiosis or red-cedar asthma
Wood asthma
495.9	Unspecified allergic alveolitis and pneumonitis
Alveolitis, allergic (extrinsic)
Hypersensitivity pneumonitis
496	Chronic airway obstruction, not elsewhere classified
Chronic:
nonspecific lung disease
obstructive lung disease
obstructive pulmonary disease [COPD] NOS
Note:	This code is not to be used with any code from categories 491-493
Excludes:	chronic obstructive lung disease [COPD] specified (as) (with):
allergic alveolitis (495.0-495.9)
asthma (493.2)
bronchiectasis (494.0-494.1)
bronchitis (491.20-491.22)
with emphysema (491.20-491.22)
decompensated (491.21)
emphysema (492.0-492.8)

PNEUMOCONIOSES AND OTHER LUNG DISEASES DUE TO EXTERNAL AGENTS (500-508)

500	Coal workers' pneumoconiosis
Anthracosilicosis
Anthracosis
Black lung disease
Coal workers' lung
Miners' asthma
501	Asbestosis
502	Pneumoconiosis due to other silica or silicates
Pneumoconiosis due to talc
Silicotic fibrosis (massive) of lung
Silicosis (simple) (complicated)
503	Pneumoconiosis due to other inorganic dust
Aluminosis (of lung)
Bauxite fibrosis (of lung)
Berylliosis
Graphite fibrosis (of lung)
Siderosis
Stannosis
504	Pneumonopathy due to inhalation of other dust
Byssinosis
Cannabinosis
Flax-dressers' disease
Excludes:	allergic alveolitis (495.0-495.9)
asbestosis (501)
bagassosis (495.1)
farmers' lung (495.0)
505	Pneumoconiosis, unspecified
506	Respiratory conditions due to chemical fumes and vapors
Use additional E code to identify cause
506.0	Bronchitis and pneumonitis due to fumes and vapors
Chemical bronchitis (acute)
506.1	Acute pulmonary edema due to fumes and vapors
Chemical pulmonary edema (acute)
Excludes:	acute pulmonary edema NOS (518.4)
chronic or unspecified pulmonary edema (514)
506.2	Upper respiratory inflammation due to fumes and vapors
506.3	Other acute and subacute respiratory conditions due to fumes and vapors
506.4	Chronic respiratory conditions due to fumes and vapors
Emphysema (diffuse) (chronic) due to inhalation of chemical fumes and vapors
Obliterative bronchiolitis (chronic) (subacute) due to inhalation of chemical fumes and
 vapors
Pulmonary fibrosis (chronic) due to inhalation of chemical fumes and vapors
506.9	Unspecified respiratory conditions due to fumes and vapors
Silo-fillers' disease
507	Pneumonitis due to solids and liquids
Excludes:	fetal aspiration pneumonitis (770.18)
507.0	Due to inhalation of food or vomitus
Aspiration pneumonia (due to):
NOS
food (regurgitated)
gastric secretions
milk
saliva
vomitus
507.1	Due to inhalation of oils and essences
Lipoid pneumonia (exogenous)
Excludes:	endogenous lipoid pneumonia (516.8)
507.8	Due to other solids and liquids
Detergent asthma
508	Respiratory conditions due to other and unspecified external agents
Use additional E code to identify cause
508.0	Acute pulmonary manifestations due to radiation
Radiation pneumonitis
508.1	Chronic and other pulmonary manifestations due to radiation
Fibrosis of lung following radiation
508.8	Respiratory conditions due to other specified external agents
508.9	Respiratory conditions due to unspecified external agent

OTHER DISEASES OF RESPIRATORY SYSTEM (510-519)

510	Empyema
Use additional code to identify infectious organism (041.0-041.9)
Excludes:	abscess of lung (513.0)
510.0	With fistula
Fistula:
bronchocutaneous
bronchopleural
hepatopleural
mediastinal
pleural
thoracic
Any condition classifiable to 510.9 with fistula
510.9	Without mention of fistula
Abscess:
pleura
thorax
Empyema (chest) (lung) (pleura)
Fibrinopurulent pleurisy
Pleurisy:
purulent
septic
seropurulent
suppurative
Pyopneumothorax
Pyothorax
511	Pleurisy
Excludes:	malignant pleural effusion (197.2)
pleurisy with mention of tuberculosis, current disease (012.0)
511.0	Without mention of effusion or current tuberculosis
Adhesion, lung or pleura
Calcification of pleura
Pleurisy (acute) (sterile):
diaphragmatic
fibrinous
interlobar
Pleurisy:
NOS
pneumococcal
staphylococcal
streptococcal
Thickening of pleura
511.1	With effusion, with mention of a bacterial cause other than tuberculosis
Pleurisy with effusion (exudative) (serous):
pneumococcal
staphylococcal
streptococcal
other specified nontuberculous bacterial cause
511.8	Other specified forms of effusion, except tuberculous
Encysted pleurisy
Hemopneumothorax
Hemothorax
Hydropneumothorax
Hydrothorax
Excludes:	traumatic (860.2-860.5, 862.29, 862.39)
511.9	Unspecified pleural effusion
Pleural effusion NOS
Pleurisy:
exudative
serofibrinous
serous
with effusion NOS
512	Pneumothorax
512.0	Spontaneous tension pneumothorax
512.1	Iatrogenic pneumothorax
Postoperative pneumothorax
512.8	Other spontaneous pneumothorax
Pneumothorax:
NOS
acute
chronic
Excludes:	pneumothorax:
congenital (770.2)
traumatic (860.0-860.1, 860.4-860.5)
tuberculous, current disease (011.7)
513	Abscess of lung and mediastinum
513.0	Abscess of lung
Abscess (multiple) of lung
Gangrenous or necrotic pneumonia
Pulmonary gangrene or necrosis
513.1	Abscess of mediastinum
514	Pulmonary congestion and hypostasis
Hypostatic:
bronchopneumonia
pneumonia
Passive pneumonia
Pulmonary congestion (chronic) (passive)
Pulmonary edema:
NOS
chronic
Excludes:	acute pulmonary edema:
NOS (518.4)
with mention of heart disease or failure (428.1)
hypostatic pneumonia due to or specified as a specific type of pneumonia - code to the type
 of pneumonia
 (480.0-480.9, 481, 482.0-482.9, 483.0-483.8, 485, 486, 487.0)
515	Postinflammatory pulmonary fibrosis
Cirrhosis of lung chronic or unspecified
Fibrosis of lung (atrophic) (confluent) (massive) (perialveolar) (peribronchial) chronic
 or unspecified
Induration of lung chronic or unspecified
516	Other alveolar and parietoalveolar pneumonopathy
516.0	Pulmonary alveolar proteinosis
516.1	Idiopathic pulmonary hemosiderosis
Essential brown induration of lung
Code first underlying disease (275.0)
516.2	Pulmonary alveolar microlithiasis
516.3	Idiopathic fibrosing alveolitis
Alveolar capillary block
Diffuse (idiopathic) (interstitial) pulmonary fibrosis
Hamman-Rich syndrome
516.8	Other specified alveolar and parietoalveolar pneumonopathies
Endogenous lipoid pneumonia
Interstitial pneumonia (desquamative) (lymphoid)
Excludes:	lipoid pneumonia, exogenous or unspecified (507.1)
516.9	Unspecified alveolar and parietoalveolar pneumonopathy
517	Lung involvement in conditions classified elsewhere
Excludes:	rheumatoid lung (714.81)
517.1	Rheumatic pneumonia
Code first underlying disease (390)
517.2	Lung involvement in systemic sclerosis
Code first underlying disease (710.1)
517.3	Acute chest syndrome
Code first sickle-cell disease in crisis (282.42, 282.62, 282.64, 282.69)
517.8	Lung involvement in other diseases classified elsewhere
Code first underlying disease, as:
amyloidosis (277.30-277.39)
polymyositis (710.4)
sarcoidosis (135)
Sj�gren's disease (710.2)
systemic lupus erythematosus (710.0)
Excludes:	syphilis (095.1)
518	Other diseases of lung
518.0	Pulmonary collapse
Atelectasis
Collapse of lung
Middle lobe syndrome
Excludes:	atelectasis:
congenital (partial) (770.5)
primary (770.4)
tuberculous, current disease (011.8)
518.1	Interstitial emphysema
Mediastinal emphysema
Excludes:	surgical (subcutaneous) emphysema (998.81)
that in fetus or newborn (770.2)
traumatic emphysema (958.7)
518.2	Compensatory emphysema
518.3	Pulmonary eosinophilia
Eosinophilic asthma
L�ffler's syndrome
Pneumonia:
allergic
eosinophilic
Tropical eosinophilia
518.4	Acute edema of lung, unspecified
Acute pulmonary edema NOS
Pulmonary edema, postoperative
Excludes:	pulmonary edema:
acute, with mention of heart disease or failure (428.1)
chronic or unspecified (514)
due to external agents (506.0-508.9)
518.5	Pulmonary insufficiency following trauma and surgery
Adult respiratory distress syndrome
Pulmonary insufficiency following:
shock
surgery
trauma
Shock lung
Excludes: adult respiratory distress syndrome associated with other conditions (518.82)
pneumonia:
aspiration (507.0)
hypostatic (514)
respiratory failure in other conditions (518.81, 518.83-518.84)
518.6	Allergic bronchopulmonary aspergillosis
518.7	Transfusion related acute lung injury (TRALI)
518.8	Other diseases of lung
518.81	Acute respiratory failure
Respiratory failure NOS
Excludes:	acute and chronic respiratory failure (518.84)
acute respiratory distress (518.82)
chronic respiratory failure (518.83)
respiratory arrest (799.1)
respiratory failure, newborn (770.84)
518.82	Other pulmonary insufficiency, not elsewhere classified
Acute respiratory distress
Acute respiratory insufficiency
Adult respiratory distress syndrome NEC
Excludes: adult respiratory distress syndrome associated with trauma or surgery (518.5)
pulmonary insufficiency following trauma or surgery (518.5)
respiratory distress:
NOS (786.09)
newborn (770.89)
syndrome, newborn (769)
shock lung (518.5)
518.83	Chronic respiratory failure
518.84	Acute and chronic respiratory failure
Acute on chronic respiratory failure
518.89	Other diseases of lung, not elsewhere classified
Broncholithiasis
Calcification of lung
Lung disease NOS
Pulmolithiasis
519	Other diseases of respiratory system
519.0	Tracheostomy complications
519.00	Tracheostomy complication, unspecified
519.01	Infection of tracheostomy
Use additional code to identify type of infection, such as:
abscess or cellulitis of neck (682.1)
septicemia (038.0-038.9)
Use additional code to identify organism (041.00-041.9)
519.02	Mechanical complication of tracheostomy
Tracheal stenosis due to tracheostomy
519.09	Other tracheostomy complications
Hemorrhage due to tracheostomy
Tracheoesophageal fistula due to tracheostomy
519.1	Other diseases of trachea and bronchus, not elsewhere classified
519.11	Acute bronchospasm
Bronchospasm NOS
Excludes:	acute bronchitis with bronchospasm (466.0)
asthma (493.00 - 493.92)
exercise induced bronchospasm (493.81)
519.19	Other diseases of trachea and bronchus
Calcification of bronchus or trachea
Stenosis of bronchus or trachea
Ulcer of bronchus or trachea
519.2	Mediastinitis
519.3	Other diseases of mediastinum, not elsewhere classified
Fibrosis of mediastinum
Hernia of mediastinum
Retraction of mediastinum
519.4	Disorders of diaphragm
Diaphragmitis
Paralysis of diaphragm
Relaxation of diaphragm
Excludes:	congenital defect of diaphragm (756.6)
diaphragmatic hernia (551-553 with .3)
congenital (756.6)
519.8	Other diseases of respiratory system, not elsewhere classified
519.9	Unspecified disease of respiratory system
Respiratory disease (chronic) NOS







TABLE OF CONTENTS

Preface

Acknowledgments

Introduction

The ICD-9-CM Coordination and Maintenance Committee

Characteristics of the ICD-9-CM

The Disease Classification

Alphabetical Index of Diseases

Table of Drugs and Chemicals

Index To External Causes of Injury (E Code)

Classification of Procedures

Index to Procedures

Appendix A:
Morphology of Neoplasms


Appendix C:
Classification of Drugs by American Hospital Formulary Services List Number and their ICD-9-CM Equivalents


Appendix D:
Classification of Industrial Accidents According to Agency


Appendix E:
List of Three-Digit Categories






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